VOLUME 31 - NUMBER 8-9 - 2010

Papillary glioneuronal tumor of the fourth ventricle: case report and review of the literature


  • Ulivieri S., Oliveri G., Cerase A., Miracco C.
  • Casistica clinica, 368-370
  • Full text PDF

  • Versione Italiana: Il tumore glioneuronale del quarto ventricolo è un’entità antomo-patologica di recente definizione e in letteratura sono riportati, ad oggi, solo 17 casi. Gli Autori presentano la loro esperienza e pongono l’attenzione ai dati morfologici e immunoistochimici della lesione revisionando la letteratura pertinente.

    English version: Rosette-forming glioneuronal tumour (RGNT) of the fourth ventricle is a relatively new entity recently described. Neuronal and mixed neuronal-glial tumours have been incorporated in the same category in the WHO Classification of Nervous System Tumours. This category comprises heterogenous neoplasms composed of neuronal and glial cells with various grades of differentiation. We present a case of papillary glioneuronal tumor occurring in a 44-year-old man with an unusual hemorrhagic onset. The clinical, morphological and immunohistochemical features are discussed and the published literature is reviewed.

  • KEY WORDS: Fourth ventricle - Central nervous system - Intracerebral haemorrhage - Glioneuronal tumor. Quarto ventricolo - Sistema nervoso centrale - Emorragia cerebrale - Tumore glioneuronale.